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Figure 1

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Structure des micro et mini-dystrophines (d’après [3]). A Isoformes naturelles. Les transcrits Dp427 ont 3 isoformes dans le cerveauDp427(B), le muscle Dp427(M) et les cellules de Purkinje Dp427(P). Des isoformes plus courtes sontproduites dans la rétine (Dp260), le cerveau etle rein (Dp140), les cellules de Schwann (Dp116). B Structure des mini- et micro-dystrophines.

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